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# Camptodactyly: Features, Classification, & Management
- URL: https://www.theplasticsfella.com/camptodactyly/
- Published: 2024-04-23T18:44:00.000Z
- Updated: 2024-04-24T18:34:36.000Z
- Description: Camptodactyly is the progressive flexion deformity of the PIPJ. This article details the aetiology, features, classification, and management of this congenital hand condition.
- Author: PlasticsFella
- Tags: Upper Limb, Paediatrics

#### Summary Card

[****Definition of Camptodactyly**](https://www.theplasticsfella.com/camptodactyly/#definition-of-camptodactyly)  
Progressive flexion deformity of the PIPJ.

[****Features of Camptodactyly**](https://www.theplasticsfella.com/camptodactyly/#features-of-camptodactyly)  
Often bilateral and little finger. An X-Ray may show secondary complications.

[****Classification of Camptodactyly**](https://www.theplasticsfella.com/camptodactyly/#classification-of-camptodactyly)  
Classified based on onset of deformity and severity of the flexion.

[****Management of Camptodactyly**](https://www.theplasticsfella.com/camptodactyly/#management-of-camptodactyly)  
Serial splinting and education for most patients. Surgery has a low success rate.   

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## Definition of Camptodactyly 

Camptodactyly is the *progressive* flexion deformity of the [proximal interphalangeal joint](https://www.theplasticsfella.com/pipj-anatomy/). Swanson classifies it as a 'failure of differentiation'. 

The image below illustrates the definition of Camptodactyly.

![Definition of Camptodactyly](https://storage.ghost.io/c/a0/9f/a09fd7b4-d396-4b28-aed3-b87e20483292/content/images/2022/08/Camptodactyly-Definition.png)

Definition of Camptodactyly

💡

****Tip:** the progressive nature of this condition is a key differentiator to arthrogryposis. 

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## Features of Camptodactyly

****Key Point**  
  
Camptodactlyly is a flexion deformity of the PIPJ that is usually the little finger and bilaterally. Radiology may show secondary sequelae. It is classified based on the onset of deformity.

### Clinical Features 

Camptodactyly is characterised by the progressive flexion deformity of the [proximal interphalangeal joint](https://www.theplasticsfella.com/pipj-anatomy/). It affects females more than males. 

Some key points include:

- Abnormal flexion posture of PIPJ.
- Painless without swelling.
- Often bilateral and involves the little finger.

Often **caused** by abnormal lumbrical insertion (HINT: pain on passive extension), short FDS tendon, and abnormal extensor mechanism. 

The **differential diagnosis** includes:

- Traumatic PIPJ injury.
- **Arthrogryposis**: congenital, ulnar deviation, multiple joints.
- **Symphalangism** (failure of joint formation) if no skin creases.
- Kirner’s deformity is not a differential diagnosis. This is a skeletal deformity characterised by progressive palmar and radial curvature of the **DIPJ**.

💡

****Tip:** Examining PIPJ extension with MCPJ flexed can differentiate between intrinsic and extrinsic causes.

The image below illustrates this failure of differentiation of Camptodactyly.

![Camptodactyly classification, Failure of Differentiation in Camptodactyly](https://storage.ghost.io/c/a0/9f/a09fd7b4-d396-4b28-aed3-b87e20483292/content/images/2022/08/Camptodactyly-features.png)

Failure of Differentiation in Camptodactyly

### Radiological Signs 

Generally speaking, an X-Ray will not show any primary cause for the camptodactyly as its aetiology is of soft tissue origin. It can show some secondary changes, such as:

- Morphological changes to the proximal phalanx.
- Decrease in proximal phalanx head convexity.
- Flattening at the base of the middle phalanx.
- Loss of [PIPJ](https://www.theplasticsfella.com/pipj-anatomy/) joint space with volar subluxation.

Check out the below image for the X-ray view of Camptodactyly.

![Camptodactyly X-ray view](https://storage.ghost.io/c/a0/9f/a09fd7b4-d396-4b28-aed3-b87e20483292/content/images/2022/08/Xray-of-Camptodactyly.png)

X-ray representation of Camptodactyly

💡

****Tip:** a flattened dorsal phalanx is often not surgically correctable. 

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## Classification of Camptodactyly

****Key Point**  
  
Camptodactyly is classified based on onset of deformity and severity of the flexion.

Camptodactyly classification is based on the **onset** of flexion deformities. 

- **Type I:** occurs during infancy (the most common type).
- **Type II:** occurs during pre-teenage years.
- **Type III:** severe, multiple digits, associated with syndromes.

😎

****Fun Fact:** Type II camptodactyly can progress to Type III.

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## Management of Camptodactyly 

****Key Point**  
  
The majority of the patients with camptodactyly can be treated conservatively with splinting and education. Surgery is unlikely to achieve a successful outcome.

Patients with camptodactyly can be treated by conservative or surgical options. This depends on the extent of their severity. 

The majority of patients can be managed in an **outpatient setting** by:

- Education
- Physiotherapy
- Serial Splinting or casting

In a select number of patients with severe disease, **surgical** considerations can include:

- FDS transfer to extensor surface
- Angulation osteotomy
- Fusion

Surgery should be performed in a step-wise manner to release and reconstruct structures until the flexion deformity is corrected.

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## Conclusion 

## 

Upon completing this article, you will have accomplished the following:  
  
****1\. Pathophysiology of Camptodactyly:** You have learned that camptodactyly is characterized by a progressive flexion deformity of the proximal interphalangeal joint (PIPJ), predominantly affecting the little finger and often presenting bilaterally.  
  
****2\. Clinical and Radiological Features:** You are now familiar with the clinical presentation of camptodactyly, which typically includes a painless, abnormal flexion posture of the PIPJ without swelling, and how radiology can show secondary changes but not the primary cause due to its soft tissue origins.  
  
****3\. The Classification System:** You understand the classification of camptodactyly based on the onset of the deformity and the severity of the flexion for predicting the progression and planning the management strategy.  
  
****4\. Management Strategies:** You have understood the conservative management approaches such as education, physiotherapy, and serial splinting, and understand when surgical intervention might be considered, and its generally low success rate.

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